PubMed journal article [Idiopathic pulmonary hemosiderosis were found in PRIME PubMed. Download Source. Revista chilena de pediatrĂ­a pg PubMed journal article [Idiopathic pulmonary hemosiderosis: review of literature and case report were found in La Pediatria Sep 30 pg Revista Cubana de PediatrĂ­a Idiopathic pulmonary hemosiderosis is those processes characterized by anomalous depots of hemosiderin in the pulmonary.

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In this situation, therapy is often started at the stage in which pulmonary fibrosis has already developed, uemosiderosis a higher risk of complications and worse prognosis.

Severe iron-deficiency anemia as initial manifestation of pulmonary hemosiderosis in a child

A favorable prognosis may be expected in our case, as there were no major episodes of hemorrhage and response to therapy was favorable. Although they do not make the definitive diagnosis of alveolar hemorrhage, chest radiography and CT scan may present suggestive but not specific aspects of hemorrhage, additionally contributing to the exclusion of other conditions. After hemosiderosiis etiological study, the hemosiderrosis of idiopathic pulmonary hemosiderosis was made by exclusion.

Please review our privacy policy. Iron-deficiency anemia is the most frequent hematologic disease in pediatrics. Orphanet J Rare Dis. The prognosis of idiopathic PH tends to improve with age and is more favorable when the diagnosis is made before the progression to pulmonary fibrosis.

Idiopathic pulmonary hemosiderosis in an adult. J Paediatr Child Health. Subsequently, pulmonary infiltrates suggestive of alveolar hemorrhage were observed in the chest radiography. He was initiated on corticosteroid therapy, later associated to an immunosuppressive agent, with subsequent correction of anemia and of the radiological pattern. Author information Article notes Copyright and License information Disclaimer. After 3 days, he maintained fever and the chest radiograph showed a diffuse bilateral opacity with ill-defined edges, interpreted as an atypical pneumonia, and he was started on clarithromycin.


As an outpatient, he received weekly intravenous iron therapy and investigation of anemia was continued. Idiopathic pulmonary hemosiderosis – a diagnostic challenge. He was transfused with packed red blood cells and was admitted for pfdiatria and investigation. pedistria

Severe iron-deficiency anemia as initial manifestation of pulmonary hemosiderosis in a child

Foi iniciado tratamento com oxacilina e azitromicina. Contudo, o acompanhamento da paciente por quatro anos afastou estas possibilidades, bem como a possibilidade de colagenoses e vasculites. SRJ is a prestige metric based on the idea that not all hemosiderpsis are the same.

Favourable response to azathioprine. Chloroquine in idiopathic pulmonary hemosiderosis. Idiopathic pulmonary hemosiderosis in a 9-year-old girl. Vitamin B 12 and folic acid were within normal range and the bone marrow smear was compatible with sideropenia. No dia seguinte, mantinha-se grave, com piora do hemograma Hct: A physician survey reveals differences in management of idiopathic pulmonary hemosiderosis.

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Five days after being discharged, he was seen again for fever, asthenia, coryza, and productive cough. Idiopathic pulmonary hemosiderosis is a potentially fatal disease that results from episodes of alveolar hemorrhage of unknown origin. The patient is currently asymptomatic. SNIP measures contextual citation impact by wighting citations based on the total number of citations in a subject field.

Abdominopelvic ultrasound, gastroduodenal and intestinal series, intestinal scintigraphy and enteral magnetic resonance imaging were normal. A pulmonary computerized tomography CT scan Figure 3 showed diffuse ground-glass attenuation in both lungs with no zonal predilection, some dispersed areas of lower density, and several scattered micronodules. Pediatr Rio de J. Open in a separate window. Subscribe to our Newsletter. After 6 days, he was discharged on oral iron therapy, with Hb of 8.


However, the latter may also present acutely with massive and potentially fatal hemoptysis.

Idiopathic pulmonary hemosiderosis: radiological findings in ..|INIS

Upper and lower gastrointestinal endoscopies with biopsies were performed and no hemorrhagic lesion was found, and the mucosa was macroscopically and histologically normal.

There are no universal recommendations regarding treatment of idiopathic PH. Pulmonary haemosiderosis in infants and children. The coproculture, parasite stool exam and fecal occult blood test were negative.

Acute respiratory insufficiency as debut of idiopathic pulmonary hemosiderosis in an infant. Diffuse increase of the parenchyma’s density with no zone predominance, with dispersed areas of lower density, and several small dispersed nodules.

Pulmonary hemorrhage can also be confirmed by the identification of hemosiderin-laden macrophages hemosideerosis the bronchoalveolar lavage fluid.

[Hydroxychloroquine in pediatric idiopathic pulmonary hemosiderosis–a case report].

Gastrointestinal bleeding was ruled out after negative extensive etiological investigation. Anemia might be the only manifestation of PH, preceding any other symptom and sign by several months.

Chest computerized tomography scan. There were no morphologic abnormalities or changes of the respiratory mucosa, and the cytological exam of the bronchoalveolar lavage showed You can change the settings or obtain more information by clicking here. On the other hand, the rarity of the alveolar hemorrhage and the variability of the clinical course frequently result in a delay in the diagnosis. This is an Open Hemsoiderosis article distributed under the terms of the Creative Commons Attribution Non-Commercial License, which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

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